Simunovic · Eye (London, England) 2010 · narrative review · n=?

Colour vision deficiency.

Cited 273 times in the scientific literature.

Level 5 - mechanism / opinion, no new human data

Narrative review without systematic search or meta-analysis

PubMed 19927164 · doi:10.1038/eye.2009.251 · record verified 2026-08-26

What was done

This narrative review summarizes the pathophysiology, genetic mechanisms, prevalence, and clinical management of congenital and acquired colour vision deficiencies based on behavioural data, modern molecular genetics, and emerging experimental treatments.

What was found

Congenital colour vision deficiency affects up to 8% of males and 0.5% of females, reflecting an X-linked recessive inheritance pattern for the most common forms. Management currently relies primarily on counseling, including career guidance. The review notes that while visual aids can assist with certain specific tasks, evidence indicates they do not enable individuals to achieve normal colour discrimination. Animal models of gene therapy have demonstrated improvement following treatment.

Why it matters

It provides clinicians with a concise overview of the epidemiology, molecular genetics, and realistic expectations regarding assistive devices and future therapeutic avenues for colour vision deficiency.

Limits

This is a broad narrative review that presents general epidemiology and mechanism-based summaries without reporting a systematic literature search, formal quality assessment of included studies, sample sizes, or quantitative effect estimates for visual aids.

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