Van Rij · European journal of human genetics : EJHG 2012 · multicentre prospective cohort study · n=331 couples

Preimplantation genetic diagnosis (PGD) for Huntington's disease: the experience of three European centres.

Cited 61 times in the scientific literature.

Level 4 - case-series / case-control

Uncontrolled prospective multicentre case series

PubMed 22071896 · doi:10.1038/ejhg.2011.202 · record verified 2026-08-26

What was done

Prospective cohort study analyzing 13 years (1995–2008) of preimplantation genetic diagnosis (PGD) for Huntington's disease (HD) across three European centres (Brussels, Maastricht, and Strasbourg). Data were collected on 331 couples at intake, evaluating reproductive history, testing method (direct CAG-triplet repeat testing vs. exclusion testing via linkage analysis), treatment cycles, and delivery outcomes.

What was found

Of 331 couples at intake, 68% requested direct testing and 32% exclusion testing. Overall, 39% of women had a previous pregnancy; history of pregnancy termination after prenatal diagnosis was significantly higher in the direct testing group (25%) than the exclusion group (10%; P=0.0027). A total of 257 couples started workup, and 174 completed at least one PGD cycle. Across 389 cycles reaching oocyte retrieval (OR), delivery rates were 19.8% per OR and 24.8% per embryo transfer, resulting in 77 deliveries and 90 live-born children.

Why it matters

This study provides multi-centre benchmark data on the feasibility, intake patterns, and delivery rates of direct and exclusion PGD for couples at risk of transmitting Huntington's disease.

Limits

The study is an uncontrolled observational series from specialized European centres. The abstract does not report diagnostic error rates, miscarriage rates, adverse pregnancy outcomes, or long-term pediatric follow-up data.

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