Kuczynska · Cells 2021 · narrative review · n=?

Covering the Role of PGC-1α in the Nervous System.

Cited 39 times in the scientific literature.

Level 5 - mechanism / opinion, no new human data

Narrative review of mechanistic, cell-culture, and animal model studies.

PubMed 35011673 · doi:10.3390/cells11010111 · record verified 2026-08-28

What was done

Narrative review of recent literature examining the roles of the transcriptional coactivator PGC-1α (peroxisome proliferator-activated receptor-γ coactivator-1α) and its CNS-specific isoforms across different neuronal and glial cell types.

What was found

The abstract reports no numerical data. It summarizes preclinical findings indicating that PGC-1α deficiency in mice impairs interneuron and dopaminergic neuron viability, inhibitory signaling, and behavior. Across rodent models, PGC-1α protects upper motoneurons in ALS models, aids lower motoneuron neuromuscular junction formation, reduces sensory neuron oxidative stress, and protects photoreceptors. In glial lineages, it is implicated in astrocyte maturation and proliferation, oligodendrocyte myelination, and microglial autophagy/mitophagy, alongside developmental and postnatal synaptogenesis.

Why it matters

Understanding the diverse, cell-type-specific functions of PGC-1α in the brain clarifies its mechanistic role in neurodegenerative pathophysiology and identifies pathways for potential therapeutic targeting.

Limits

The review relies on rodent and in vitro models without human clinical data. As a narrative review, it lacks systematic search methodology, risk-of-bias assessment, and quantitative effect sizes.

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