Rey · Bailliere's clinical endocrinology and metabolism 1998 · narrative review · n=?

Embryology and endocrinology of genital development.

Cited 110 times in the scientific literature.

Level 5 - mechanism / opinion, no new human data

Narrative review summarizing biological mechanisms without systematic review methodology or new human data.

PubMed 9890060 · doi:10.1016/s0950-351x(98)80427-8 · record verified 2026-08-26

What was done

This narrative review summarizes the embryological and hormonal mechanisms governing human fetal sexual differentiation, focusing on the roles of anti-müllerian hormone (AMH), testosterone, and dihydrotestosterone (DHT), as well as the genetic basis of persistent müllerian duct syndrome.

What was found

The abstract reports no numerical or quantitative data. It details the established physiological sequence: fetal testes develop by week 7 and secrete AMH to regress müllerian ducts and testosterone to differentiate wolffian ducts into epididymes, vasa deferentia, and seminal vesicles. Conversion of testosterone to DHT drives masculinization of the urogenital sinus and external genitalia. In the absence of AMH and androgen action, female internal and external genitalia develop. Mutations in AMH or its receptor gene impair this pathway, leading to persistent müllerian duct syndrome in otherwise virilized males.

Why it matters

It outlines the dual hormonal control required for male sexual differentiation and highlights the specific genetic lesions underlying persistent müllerian duct syndrome.

Limits

The abstract provides a descriptive overview with no empirical data, sample size, or systematic methodology. It does not evaluate clinical outcomes, diagnostic accuracy, or non-genetic contributors to disorders of sex development.

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